Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clingen Thrombosis Variant Curation Expert Panel, |
RCV002145366 | SCV005442759 | uncertain significance | Hereditary antithrombin deficiency | 2024-10-02 | reviewed by expert panel | curation | The c.1275T>C (NM_000488.4) variant in SERPINC1 does not code for a different amino acid (p.Arg425=). SpliceAI predicts no splicing impact for this variant meeting BP4. The variant is reported at a POPMAX FAF of 0.000008797 (1/113670) in the European population in gnomAD v2.1.1 which meets PM2_supporting criteria (MAF < 2.0 X 10-5 in gnomAD). In summary, based on the evidence available at this time, the clinical significance of this variant is uncertain. ACMG/AMP criteria applied, as specified by the Thrombosis Variant Curation Expert Panel for SERPINC1: BP4, PM2_supporting. |
Labcorp Genetics |
RCV002145366 | SCV002422989 | likely benign | Hereditary antithrombin deficiency | 2021-08-01 | criteria provided, single submitter | clinical testing |