Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clingen Thrombosis Variant Curation Expert Panel, |
RCV003330313 | SCV004037400 | likely benign | Hereditary antithrombin deficiency | 2023-07-25 | reviewed by expert panel | curation | The variant is reported at the highest MAF of 0.00004412 (5/113318 alleles) in the non-Finnish European population, which does not meet criteria for PM2_Supporting. This variant has not been reported in the literature in association with autosomal dominant antithrombin III deficiency. The variant is reported in 2 individuals in internal cohort, with 1 reporting normal antithrombin levels meeting BS2_supporting. The variant has a REVEL score of 0.127, which does meet criteria for BP4 (SpliceAI and VarSEAK predicts no impact). In summary, this variant meets criteria to be classified as likely benign. ACMG/AMP criteria applied, as specified by the Thrombosis Variant Curation Expert Panel for SERPINC1: BS2_supporting, BP4. |
Hubei Clinical and Research Center of Thrombosis and Hemostasis Institute of Hematology, |
RCV000144053 | SCV000189124 | not provided | not provided | no assertion provided | not provided |