Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001235205 | SCV001407881 | pathogenic | Alpha thalassemia-X-linked intellectual disability syndrome | 2019-09-16 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in ATRX are known to be pathogenic (PMID: 18409179, 23681356). This variant has not been reported in the literature in individuals with ATRX-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Lys1357*) in the ATRX gene. It is expected to result in an absent or disrupted protein product. |