Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV000995969 | SCV001150383 | uncertain significance | not provided | 2019-01-01 | criteria provided, single submitter | clinical testing | |
Institute of Human Genetics, |
RCV001253370 | SCV001429049 | likely pathogenic | Alpha thalassemia-X-linked intellectual disability syndrome | 2018-10-02 | criteria provided, single submitter | clinical testing | This variant was identified as hemizygous |
Gene |
RCV000995969 | SCV002006696 | uncertain significance | not provided | 2019-05-30 | criteria provided, single submitter | clinical testing | Not observed in large population cohorts (Lek et al., 2016); Has not been previously published as pathogenic or benign to our knowledge; In silico analysis, which includes splice predictors and evolutionary conservation, suggests this variant may impact gene splicing. In the absence of RNA/functional studies, the actual effect of this sequence change is unknown |