Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000029510 | SCV003497493 | pathogenic | Cystic fibrosis | 2022-01-20 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 35855). This sequence change creates a premature translational stop signal (p.Lys978*) in the CFTR gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CFTR are known to be pathogenic (PMID: 1695717, 7691345, 9725922). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with CFTR-related conditions. For these reasons, this variant has been classified as Pathogenic. |
Baylor Genetics | RCV003473136 | SCV004213499 | pathogenic | Bronchiectasis with or without elevated sweat chloride 1 | 2023-05-23 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000029510 | SCV000052161 | likely pathogenic | Cystic fibrosis | 2015-10-02 | no assertion criteria provided | clinical testing | |
Counsyl | RCV000029510 | SCV000798430 | likely pathogenic | Cystic fibrosis | 2018-03-05 | no assertion criteria provided | clinical testing | |
Natera, |
RCV000029510 | SCV001461251 | likely pathogenic | Cystic fibrosis | 2020-09-16 | no assertion criteria provided | clinical testing |