Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000757866 | SCV000886379 | uncertain significance | Cystic fibrosis | 2018-11-05 | criteria provided, single submitter | clinical testing | |
MGZ Medical Genetics Center | RCV002290003 | SCV002580977 | uncertain significance | Hereditary pancreatitis | 2022-07-14 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000757866 | SCV005559880 | uncertain significance | Cystic fibrosis | 2024-07-11 | criteria provided, single submitter | clinical testing | The p.L1040F variant (also known as c.3118C>T), located in coding exon 19 of the CFTR gene, results from a C to T substitution at nucleotide position 3118. The leucine at codon 1040 is replaced by phenylalanine, an amino acid with highly similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |