Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV003004834 | SCV003714518 | uncertain significance | Inborn genetic diseases | 2022-09-22 | criteria provided, single submitter | clinical testing | The c.1240C>G (p.P414A) alteration is located in exon 8 (coding exon 8) of the CYP11B1 gene. This alteration results from a C to G substitution at nucleotide position 1240, causing the proline (P) at amino acid position 414 to be replaced by an alanine (A). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Zotz- |
RCV003333809 | SCV004041781 | uncertain significance | Deficiency of steroid 11-beta-monooxygenase | 2023-10-09 | no assertion criteria provided | clinical testing |