Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostics Laboratory, |
RCV002236395 | SCV002507310 | likely pathogenic | Hereditary factor X deficiency disease | 2021-12-22 | criteria provided, single submitter | clinical testing | |
OMIM | RCV002267785 | SCV000045368 | pathogenic | Factor X deficiency | 2000-02-01 | no assertion criteria provided | literature only | |
Prevention |
RCV004731246 | SCV005335372 | likely pathogenic | F10-related disorder | 2024-04-01 | no assertion criteria provided | clinical testing | The F10 c.1073C>T variant is predicted to result in the amino acid substitution p.Thr358Met. This variant (also known as p.Thr318Met using Legacy nomenclature) has been reported in the homozygous and compound heterozygous state in individuals with Factor X deficiency. Functional studies also indicate this variant impacts Factor X activity (Patient B, Odom et al. 1994. PubMed ID: 8028609; Table 1, Millar et al. 2000. PubMed ID: 10746568). This variant is reported in 0.0033% of alleles in individuals of South Asian descent in gnomAD. This variant is interpreted as likely pathogenic. |