Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV002284169 | SCV002573749 | pathogenic | not provided | 2022-01-14 | criteria provided, single submitter | clinical testing | PM1, PM2, PS3, PS4_moderate |
Gene |
RCV002284169 | SCV005689889 | pathogenic | not provided | 2024-08-07 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect on secretion (PMID: 1939653); In silico analysis indicates that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 1939653, 20331754, 26891460, 35059555, 18403394, 30507709, 37647632) |
OMIM | RCV000012838 | SCV000033078 | pathogenic | Factor X deficiency | 1993-03-15 | no assertion criteria provided | literature only |