Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Diagnosis and Therapy of Lysosomal Disorders, |
RCV001578357 | SCV001547580 | uncertain significance | Mucopolysaccharidosis, MPS-IV-A | 2021-02-01 | criteria provided, single submitter | curation | Absent from gnomAD v2.1.1 (PM2_moderate); multiple lines of computational evidence support a deleterious effect on the gene (PP3_supporting) |
Revvity Omics, |
RCV001578357 | SCV003808582 | uncertain significance | Mucopolysaccharidosis, MPS-IV-A | 2022-04-28 | criteria provided, single submitter | clinical testing | |
Molecular Biology Laboratory, |
RCV001578357 | SCV004012877 | pathogenic | Mucopolysaccharidosis, MPS-IV-A | no assertion criteria provided | research |