Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Kasturba Medical College, |
RCV001806425 | SCV002054013 | uncertain significance | Mucopolysaccharidosis, MPS-IV-A | 2022-05-09 | criteria provided, single submitter | clinical testing | |
Foundation for Research in Genetics and Endocrinology, |
RCV001806425 | SCV002754469 | uncertain significance | Mucopolysaccharidosis, MPS-IV-A | criteria provided, single submitter | clinical testing | A Hemozygous missense variation in exon 12 of the GALNS gene that results in the amino acid substitution of Isoleucine for threonine at codon 429 was detected. The observed variant c.14286C>T (p.Thr429Ile) has not been reported in the 1000 genomes and has MAF of 0.0008% in the gnomAD databases. The in silico prediction of the variant is probably damaging by SIFT and MutationTaster2. The reference codon is conserved across species. In summary, the variant meets our criteria to be classified as a variant of uncertain significance. |