Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Foundation for Research in Genetics and Endocrinology, |
RCV003222545 | SCV003915846 | likely pathogenic | Mucopolysaccharidosis, MPS-IV-A | 2023-04-13 | criteria provided, single submitter | clinical testing | A Heterozygous missense variation in intron 14 of the GALNS gene was detected. The observed variant c.1483-2A>C has not been reported in the 1000 genomes and gnomAD databases. The in silico prediction of the variant is disease causing by MutationTaster. The reference codon is conserved across species. In summary, the variant meets our criteria to be classified as likely pathogenic. |