Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV001817674 | SCV002072221 | likely pathogenic | not provided | 2017-09-21 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001817674 | SCV005079272 | likely pathogenic | not provided | 2023-11-28 | criteria provided, single submitter | clinical testing | Apparently de novo variant in a patient with pseudohypoparathyroidism type Ia in the published published literature (PMID: 29095814, 35296306); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 29095814, 35296306) |