Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV003314468 | SCV004013853 | likely pathogenic | Pseudohypoparathyroidism type I A | criteria provided, single submitter | clinical testing | The splice variant is not observed in the gnomAD v2.1.1 dataset. This variant at canonical splice site is predicted to alter splicing and result in a loss or disruption of normal protein function. Multiple pathogenic loss-of-function variants are reported downstream of the variant. Therefore, this variant is classified as likely pathogenic according to the recommendation of ACMG/AMP guideline. |