Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center of Genomic medicine, |
RCV000234886 | SCV000292231 | likely pathogenic | Hyperinsulinemic hypoglycemia, familial, 2 | 2015-03-16 | criteria provided, single submitter | clinical testing | This recessive mutation in the KCNJ11 gene was found in a case of congenital hyperinsulinemic hypoglycemia. The combination of this mutation with a second recessive mutation (c.440T>C) in the same gene explains the phenotype of this newborn patient. |
Clinical Genomics, |
RCV002226700 | SCV002505470 | uncertain significance | Maturity onset diabetes mellitus in young | criteria provided, single submitter | research | Mutations in KCNJ11 gene can cause decreased production and secretion of insulin. This can lead to MODY which may be responsive to oral sulfonylureas. It is also associated with Neonatal Diabetes. However, no sufficient evidence is found to ascertain the role of rs879253757 variant in MODY yet. | |
Baylor Genetics | RCV004567770 | SCV005059788 | pathogenic | Type 2 diabetes mellitus | 2024-02-08 | criteria provided, single submitter | clinical testing |