Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002694044 | SCV003729830 | uncertain significance | Inborn genetic diseases | 2022-01-13 | criteria provided, single submitter | clinical testing | The c.973C>T (p.R325C) alteration is located in exon 1 (coding exon 1) of the KCNJ11 gene. This alteration results from a C to T substitution at nucleotide position 973, causing the arginine (R) at amino acid position 325 to be replaced by a cysteine (C). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV005047383 | SCV005676602 | uncertain significance | Diabetes mellitus, transient neonatal, 3; Hyperinsulinemic hypoglycemia, familial, 2; Type 2 diabetes mellitus; Maturity-onset diabetes of the young type 13; Diabetes mellitus, permanent neonatal 2 | 2024-06-06 | criteria provided, single submitter | clinical testing |