Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
LDLR- |
RCV000237390 | SCV000294400 | uncertain significance | Hypercholesterolemia, familial, 1 | 2016-03-25 | criteria provided, single submitter | literature only | |
Fundacion Hipercolesterolemia Familiar | RCV000237390 | SCV000607399 | uncertain significance | Hypercholesterolemia, familial, 1 | 2016-03-01 | criteria provided, single submitter | research | |
Ai |
RCV002223825 | SCV002502553 | uncertain significance | not provided | 2021-10-21 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV003581591 | SCV004358460 | uncertain significance | Familial hypercholesterolemia | 2023-05-02 | criteria provided, single submitter | clinical testing | This variant is located in the 5' untranslated region of the LDLR gene. An in-vitro functional study has shown that this variant may not affect LDLR promoter activity (PMID: 31395865). This variant has been reported in an individual affected with familial hypercholesterolemia (PMID: 15241806). This variant has been identified in 3/279652 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |