Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV000589889 | SCV000697188 | uncertain significance | not provided | 2017-04-25 | criteria provided, single submitter | clinical testing | Variant summary: The LDLR c.1187-14C>T variant involves the alteration of a non-conserved intronic nucleotide. 5/5 splice prediction tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. This variant was found in 1/214534 control chromosomes in the gnomAD dataset at a frequency of 0.0000047, which does not exceed the estimated maximal expected allele frequency of a pathogenic LDLR variant (0.0012508). The variant of interest has not, to our knowledge, been reported in affected individuals via publications and/or reputable databases/clinical diagnostic laboratories. Due to the absence of clinical information and lack of functional studies, the variant is classified as a "Variant of Uncertain Significance (VUS)" until additional information becomes available. |
Labcorp Genetics |
RCV003767338 | SCV004685781 | likely benign | Familial hypercholesterolemia | 2023-05-17 | criteria provided, single submitter | clinical testing |