Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000819259 | SCV000959909 | uncertain significance | Familial hypercholesterolemia | 2021-09-01 | criteria provided, single submitter | clinical testing | This sequence change replaces aspartic acid with glutamic acid at codon 445 of the LDLR protein (p.Asp445Glu). The aspartic acid residue is highly conserved and there is a small physicochemical difference between aspartic acid and glutamic acid. This variant is not present in population databases (ExAC no frequency). This missense change has been observed in individual(s) with familial hypercholesterolemia (PMID: 7573037, 15199436). This variant is also known as p.Asp242Glu and FH-Fin-8. ClinVar contains an entry for this variant (Variation ID: 661768). Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. Experimental studies have shown that this missense change does not substantially affect LDLR function (PMID: 31587492). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV002487822 | SCV002778398 | uncertain significance | Hypercholesterolemia, familial, 1 | 2021-07-30 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV002487822 | SCV006057244 | uncertain significance | Hypercholesterolemia, familial, 1 | 2020-05-26 | criteria provided, single submitter | research | |
Natera, |
RCV000819259 | SCV002086417 | uncertain significance | Familial hypercholesterolemia | 2020-08-24 | no assertion criteria provided | clinical testing |