Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001189541 | SCV001356851 | uncertain significance | Familial hypercholesterolemia | 2019-04-27 | criteria provided, single submitter | clinical testing | This intronic variant changes a single nucleotide near intron 2 splice acceptor site of the LDLR gene. Computational splicing tools suggest that this variant may disrupt RNA splicing. To our knowledge, functional assays have not been performed for this variant nor has this variant been reported in individuals affected with familial hypercholesterolemia in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). Available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |