Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Diagnostic Laboratory for Inherited Cardiovascular Disease, |
RCV001256971 | SCV001433514 | likely pathogenic | not provided | 2019-11-16 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002411918 | SCV002719787 | pathogenic | Cardiovascular phenotype | 2022-09-30 | criteria provided, single submitter | clinical testing | The p.L641* pathogenic mutation (also known as c.1922T>A), located in coding exon 13 of the LDLR gene, results from a T to A substitution at nucleotide position 1922. This changes the amino acid from a leucine to a stop codon within coding exon 13. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |