Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV003163918 | SCV003866480 | uncertain significance | Cardiovascular phenotype | 2024-11-21 | criteria provided, single submitter | clinical testing | The p.Q660H variant (also known as c.1980G>C), located in coding exon 13 of the LDLR gene, results from a G to C substitution at nucleotide position 1980. The glutamine at codon 660 is replaced by histidine, an amino acid with highly similar properties. This alteration has been reported as compound heterozygous with additional alterations in LDLR in individuals reported to have familial hypercholesterolemia (FH) (Du Z et al. iScience, 2022 Nov;25:105334). This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
The Key Laboratory of Remodeling–Related Cardiovascular Diseases, |
RCV002227547 | SCV002014610 | pathogenic | Hypercholesterolemia, familial, 1 | 2019-11-30 | no assertion criteria provided | clinical testing |