Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV001178332 | SCV001342738 | uncertain significance | Familial hypercholesterolemia | 2023-12-05 | criteria provided, single submitter | clinical testing | This missense variant (also known as p.Leu751Pro in the mature protein) replaces leucine with proline at codon 772 of the LDLR protein. Computational prediction tools and conservation analyses suggest that this variant may not impact protein function. Computational splicing tools suggest that this variant may not impact RNA splicing. To our knowledge, functional assays have not been performed for this variant nor has this variant been reported in individuals affected with familial hypercholesterolemia in the literature. This variant has been identified in 1/251452 chromosomes in the general population by the Genome Aggregation Database (gnomAD). Available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Gene |
RCV002511051 | SCV002820478 | uncertain significance | not provided | 2022-07-13 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |