Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000229645 | SCV000285025 | pathogenic | Hypercholesterolemia, familial, 1 | 2016-01-10 | criteria provided, single submitter | clinical testing | This sequence change deletes 1 nucleotide from exon 4 of the LDLR mRNA (c.379delG), causing a frameshift at codon 127. This creates a premature translational stop signal (p.Val127Serfs*79) and is expected to result in an absent or disrupted protein product. While this particular variant has not been reported in the literature, truncating variants in LDLR are known to be pathogenic (PMID: 20809525). For these reasons, this variant has been classified as Pathogenic. |
Labcorp Genetics |
RCV001382356 | SCV001581091 | pathogenic | Familial hypercholesterolemia | 2016-01-10 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. While this particular variant has not been reported in the literature, truncating variants in LDLR are known to be pathogenic (PMID: 20809525). This sequence change deletes 1 nucleotide from exon 4 of the LDLR mRNA (c.379delG), causing a frameshift at codon 127. This creates a premature translational stop signal (p.Val127Serfs*79) and is expected to result in an absent or disrupted protein product. |