Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
MGZ Medical Genetics Center | RCV002288300 | SCV002579763 | uncertain significance | Lynch syndrome 4 | 2021-12-22 | criteria provided, single submitter | clinical testing | |
Institute for Human Genetics and Genomic Medicine, |
RCV002288300 | SCV004035270 | likely pathogenic | Lynch syndrome 4 | no assertion criteria provided | clinical testing | The detected alteration is not reported in the dbSNP database (dbSNP151) yet. It is not yet listed in gnomAD (as of 09/14/2023). The variant affects a Cartegni consensus splice site. Splicing prediction programs predict an impact on splicing behavior for the variant (Splice Site Finder Like (SSF): -14.5% and MaxEntScan (MES): -59.2%). In the ClinVar database, the variant has been previously reported once (in the context of HNPCC) and is classified as a "variant of unclear clinical significance" (ClinVar ID: 1707370). To our knowledge, the variant has not been previously reported in the literature in association with CMMRD Based on current knowledge, the variant should be classified as a "likely pathogenic variant" based on the ACMG criteria. (14.09.2023) |