Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV004584151 | SCV005062151 | likely pathogenic | Lynch syndrome 4 | 2024-06-28 | criteria provided, single submitter | clinical testing | The variant c.2233del (p.(Ile745Tyrfs*23)) in exon 13 of the PMS2 gene is not found in the gnomAD database and it creates a frame shift starting at codon Ile745. The new reading frame ends in a STOP codon at position 23. Frameshift variants leading to a loss of function of PMS2 protein are a known mechanism of disease. ACMG criteria used for classification: PVS1, PM2_sup. |