Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Color Diagnostics, |
RCV000775369 | SCV000909680 | uncertain significance | Hereditary cancer-predisposing syndrome | 2018-12-13 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000775369 | SCV002742721 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-06-26 | criteria provided, single submitter | clinical testing | The p.S90C variant (also known as c.269C>G), located in coding exon 4 of the PMS2 gene, results from a C to G substitution at nucleotide position 269. The serine at codon 90 is replaced by cysteine, an amino acid with dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |
Baylor Genetics | RCV003461038 | SCV004207849 | uncertain significance | Lynch syndrome 4 | 2023-05-08 | criteria provided, single submitter | clinical testing |