Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002374252 | SCV002686087 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-09-10 | criteria provided, single submitter | clinical testing | The p.Y318H variant (also known as c.952T>C), located in coding exon 9 of the PMS2 gene, results from a T to C substitution at nucleotide position 952. The tyrosine at codon 318 is replaced by histidine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
CHEO Genetics Diagnostic Laboratory, |
RCV003492759 | SCV004239608 | uncertain significance | Breast and/or ovarian cancer | 2022-09-16 | criteria provided, single submitter | clinical testing |