Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000539694 | SCV000660026 | likely benign | RYR1-related disorder | 2024-12-25 | criteria provided, single submitter | clinical testing | |
Eurofins Ntd Llc |
RCV000721652 | SCV000705063 | uncertain significance | not provided | 2017-01-13 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV000721652 | SCV000852775 | uncertain significance | not provided | 2018-06-22 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000721652 | SCV001768305 | uncertain significance | not provided | 2025-03-12 | criteria provided, single submitter | clinical testing | Previously reported as a variant of uncertain significance and identified with a second RYR1 variant in an individual with central core myopathy (PMID: 33458582); In silico analysis indicates that this missense variant does not alter protein structure/function; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 33458582) |
Revvity Omics, |
RCV000721652 | SCV003814432 | uncertain significance | not provided | 2023-05-29 | criteria provided, single submitter | clinical testing | |
Department of Pathology and Laboratory Medicine, |
RCV005398873 | SCV006058561 | uncertain significance | Central core myopathy; Malignant hyperthermia, susceptibility to, 1; Congenital multicore myopathy with external ophthalmoplegia; King Denborough syndrome | 2023-09-26 | criteria provided, single submitter | research |