Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000153870 | SCV000203464 | uncertain significance | not provided | 2014-04-10 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001078640 | SCV001092220 | benign | RYR1-related disorder | 2024-01-08 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV003998237 | SCV004823236 | likely benign | Malignant hyperthermia, susceptibility to, 1 | 2023-12-13 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004525881 | SCV005039362 | likely benign | not specified | 2024-03-13 | criteria provided, single submitter | clinical testing | Variant summary: RYR1 c.9723C>T alters a conserved nucleotide resulting in a synonymous change. Consensus agreement among computation tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant allele was found at a frequency of 8.4e-05 in 248854 control chromosomes in the gnomAD database, including 1 homozygote. This frequency does not allow for any conclusion about variant significance, but the presence of 1 homozygote may suggest a benign role for this variant. To our knowledge, no occurrence of c.9723C>T in individuals affected with Myopathy, RYR1-Associated and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 167622). Based on the evidence outlined above, the variant was classified as likely benign. |
Prevention |
RCV001078640 | SCV004713581 | likely benign | RYR1-related disorder | 2021-09-23 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |