Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000521967 | SCV000618121 | likely pathogenic | not provided | 2018-08-24 | criteria provided, single submitter | clinical testing | This variant is denoted TP53 c.128T>A at the cDNA level and p.Leu43Ter (L43X) at the protein level. The substitution creates a nonsense variant, which changes a Leucine to a premature stop codon (TTG>TAG), and is predicted to cause loss of normal protein function through either protein truncation or nonsense-mediated mRNA decay. Although this variant has not, to our knowledge, been published in the literature as a pathogenic or benign germline variant, we consider it to be likely pathogenic. |