Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV005402362 | SCV006060065 | likely pathogenic | not provided | 2024-10-23 | criteria provided, single submitter | clinical testing | Published functional studies demonstrate a damaging effect: loss of growth suppression and non-functional transcriptional activation activity (PMID: 30224644, 29979965); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 30224644, 29979965, 30661751, 15510160) |