Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Quest Diagnostics Nichols Institute San Juan Capistrano | RCV004997932 | SCV005625959 | pathogenic | not provided | 2024-04-04 | criteria provided, single submitter | clinical testing | The TP53 c.448_455del (p.Thr150Alafs*28) variant alters the translational reading frame of the TP53 mRNA and causes the premature termination of TP53 protein synthesis. This variant has not been reported in individuals with TP53-related conditions in the published literature, but it has been observed in an individual in our internal patient population affected with cancers consistent with Li-Fraumeni syndrome. This variant has not been reported in large, multi-ethnic general populations (Genome Aggregation Database, http://gnomad.broadinstitute.org). Based on the available information, this variant is classified as pathogenic. |