Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000689187 | SCV000816827 | uncertain significance | Li-Fraumeni syndrome | 2018-02-15 | criteria provided, single submitter | clinical testing | An experimental study has shown that this missense change does not affect the transcriptional transactivation activity of the TP53 protein (PMID: 12826609). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals with TP53-related disease. This variant is not present in population databases (ExAC no frequency). This sequence change replaces methionine with arginine at codon 169 of the TP53 protein (p.Met169Arg). The methionine residue is moderately conserved and there is a moderate physicochemical difference between methionine and arginine. |