Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003391538 | SCV004112281 | pathogenic | TP53-related disorder | 2023-04-24 | criteria provided, single submitter | clinical testing | The TP53 c.779_782+13del17 variant is predicted to result in a deletion affecting a canonical splice site. This deletion overlaps the exon 7/intron 7 boundary and is predicted to abolish the conical splice donor site (Alamut Visual Plus v1.6.1). To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Variants that disrupt the canonical splice donor site in TP53 are expected to be pathogenic. This variant is interpreted as pathogenic. |