Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000817259 | SCV000957809 | benign | Tuberous sclerosis 2 | 2024-09-29 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV002256079 | SCV002533328 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-11-22 | criteria provided, single submitter | curation | |
Ambry Genetics | RCV002256079 | SCV002750383 | uncertain significance | Hereditary cancer-predisposing syndrome | 2018-04-03 | criteria provided, single submitter | clinical testing | The p.S923C variant (also known as c.2768C>G), located in coding exon 24 of the TSC2 gene, results from a C to G substitution at nucleotide position 2768. The serine at codon 923 is replaced by cysteine, an amino acid with dissimilar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Gene |
RCV003148650 | SCV003836890 | uncertain significance | not provided | 2022-09-03 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Has not been previously published as pathogenic or benign to our knowledge; This variant is associated with the following publications: (PMID: 24728327) |
Neuberg Centre For Genomic Medicine, |
RCV003447498 | SCV004175828 | uncertain significance | Isolated focal cortical dysplasia type II | 2023-02-14 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV003997363 | SCV004822547 | uncertain significance | Tuberous sclerosis syndrome | 2023-06-28 | criteria provided, single submitter | clinical testing | |
ITMI | RCV000122215 | SCV000086436 | not provided | not specified | 2013-09-19 | no assertion provided | reference population |