Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000797775 | SCV000937354 | benign | Tuberous sclerosis 2 | 2024-09-10 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV003166162 | SCV003911457 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-11-18 | criteria provided, single submitter | clinical testing | The p.V986M variant (also known as c.2956G>A), located in coding exon 25 of the TSC2 gene, results from a G to A substitution at nucleotide position 2956. The valine at codon 986 is replaced by methionine, an amino acid with highly similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |
Baylor Genetics | RCV003467365 | SCV004205074 | uncertain significance | Isolated focal cortical dysplasia type II | 2023-06-06 | criteria provided, single submitter | clinical testing |