Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000475335 | SCV000544520 | benign | Tuberous sclerosis 2 | 2024-03-15 | criteria provided, single submitter | clinical testing | |
St. |
RCV000761103 | SCV000891018 | uncertain significance | Tuberous sclerosis syndrome | 2021-08-03 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000475335 | SCV002040741 | uncertain significance | Tuberous sclerosis 2 | 2021-11-07 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002436402 | SCV002753466 | uncertain significance | Hereditary cancer-predisposing syndrome | 2022-04-22 | criteria provided, single submitter | clinical testing | The p.D1013G variant (also known as c.3038A>G), located in coding exon 26 of the TSC2 gene, results from an A to G substitution at nucleotide position 3038. The aspartic acid at codon 1013 is replaced by glycine, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |