Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004680311 | SCV005181136 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-06-10 | criteria provided, single submitter | clinical testing | The c.4849+5G>C intronic variant results from a G to C substitution 5 nucleotides after coding exon 36 in the TSC2 gene. This nucleotide position is highly conserved in available vertebrate species. In silico splice site analysis predicts that this alteration will not have any significant effect on splicing. Based on the available evidence, the clinical significance of this variant remains unclear. |
All of Us Research Program, |
RCV004805135 | SCV005428355 | uncertain significance | Tuberous sclerosis syndrome | 2024-05-30 | criteria provided, single submitter | clinical testing | This variant causes a G to C nucleotide substitution at the +5 position of intron 37 of the TSC2 gene. To our knowledge, functional studies have not been reported for this variant. This variant has not been reported in individuals affected with TSC2-related disorders in the literature. This variant has not been identified in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |