Total submissions: 8
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000227246 | SCV000285425 | benign | Tuberous sclerosis 2 | 2024-02-01 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000570864 | SCV000675512 | likely benign | Hereditary cancer-predisposing syndrome | 2014-11-21 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Gene |
RCV001596996 | SCV001830429 | benign | not provided | 2015-03-03 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV000227246 | SCV002039867 | benign | Tuberous sclerosis 2 | 2021-11-07 | criteria provided, single submitter | clinical testing | |
Sema4, |
RCV000570864 | SCV002533982 | benign | Hereditary cancer-predisposing syndrome | 2021-08-24 | criteria provided, single submitter | curation | |
Color Diagnostics, |
RCV000227246 | SCV004360925 | benign | Tuberous sclerosis 2 | 2022-10-20 | criteria provided, single submitter | clinical testing | |
All of Us Research Program, |
RCV003998835 | SCV004823520 | benign | Tuberous sclerosis syndrome | 2024-02-05 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004541376 | SCV004759303 | likely benign | TSC2-related disorder | 2019-10-10 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |