Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001852883 | SCV002211581 | uncertain significance | Tuberous sclerosis 2 | 2021-08-26 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be disruptive. ClinVar contains an entry for this variant (Variation ID: 49381). This variant has not been reported in the literature in individuals affected with TSC2-related conditions. This variant is not present in population databases (ExAC no frequency). This sequence change replaces leucine with proline at codon 222 of the TSC2 protein (p.Leu222Pro). The leucine residue is highly conserved and there is a moderate physicochemical difference between leucine and proline. |
Tuberous sclerosis database |
RCV000042641 | SCV000066436 | not provided | Tuberous sclerosis syndrome | no assertion provided | curation |