Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics and Molecular Pathology, |
RCV002466947 | SCV002761930 | uncertain significance | Hereditary factor VIII deficiency disease | 2022-04-28 | criteria provided, single submitter | clinical testing | The VWF c.2308C>T variant is classified as VUS (PP3) The VWF c.2308C>T variant is a single nucleotide change in exon 18/52 of the VWF gene, which is predicted to change the amino acid proline at position 770 in the protein to serine. This variant is present at low frequency in population databases (gnomAD allele frequency = 0.0045%; 7 het and 0 hom in 152204 sequenced alleles; highest frequency = 0.096%, East Asian population) (PM2 not met). Computational predictions support a deleterious effect on the gene or gene product (PP3). The variant has been reported in dbSNP (rs149051646). It has not been reported in ClinVar or HGMD. |