Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
NIHR Bioresource Rare Diseases, |
RCV000851853 | SCV000899870 | likely pathogenic | Hereditary von Willebrand disease | 2019-02-01 | criteria provided, single submitter | research | |
Academic Unit of Haematology, |
RCV000086861 | SCV000119067 | not provided | not provided | no assertion provided | not provided | ||
Prevention |
RCV004549534 | SCV004764766 | pathogenic | VWF-related disorder | 2024-02-08 | no assertion criteria provided | clinical testing | The VWF c.6798+1G>T variant is predicted to disrupt the GT donor site and interfere with normal splicing. This variant has been reported in individuals with Von Willebrand disease 1 (James et al. 2007. PubMed ID: 17190853; Downes et al. 2019. PubMed ID: 31064749. Suppl3_SNV+INDEL). This variant is reported in 0.00088% of alleles in individuals of European (Non-Finnish) descent in gnomAD. Variants that disrupt the consensus splice donor site in VWF are expected to be pathogenic. This variant is interpreted as pathogenic. |