Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001260906 | SCV001430597 | uncertain significance | Usher syndrome | 2020-06-05 | criteria provided, single submitter | clinical testing | The CRX variant c.29A>G occurs at a frequency of 0.0008% (gnomAD). The mutation is independently classified as disease causing mutation by three prediction programs. Thus, we consider this variant to be variant of uncertain significance. ACMG criteria used for classification: PM2, PP2, BP4. |