Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000950703 | SCV001097032 | benign | MHC class I deficiency | 2025-01-28 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV000950703 | SCV002798117 | likely benign | MHC class I deficiency | 2022-03-28 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV005236471 | SCV005883971 | likely benign | not specified | 2024-12-12 | criteria provided, single submitter | clinical testing | Variant summary: TAP1 c.437C>T (p.Ala146Val) results in a non-conservative amino acid change in the encoded protein sequence. Three of four in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 0.0011 in 243084 control chromosomes, predominantly at a frequency of 0.0079 within the Latino subpopulation in the gnomAD database, including 2 homozygotes. The observed variant frequency within Latino control individuals in the gnomAD database exceeds the estimated maximal expected allele frequency for a pathogenic variant in TAP1 causing MHC Class I Deficiency phenotype. To our knowledge, no occurrence of c.437C>T in individuals affected with MHC Class I Deficiency and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 771394). Based on the evidence outlined above, the variant was classified as likely benign. |