Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001290135 | SCV001469117 | likely pathogenic | Charcot-marie-tooth disease, axonal, type 2DD | 2021-01-18 | criteria provided, single submitter | clinical testing | The variant c.2809_2819del (p.(Cys937Glufs*20)) in exon 20 of the ATP1A1-gene is not found in known databases (ExAC or gnomAD) and leads to a frameshift within the coding sequence of the ATP1A1-gene, within a protein domain, resulting in a truncated protein. Thus, we classify this variant as a likely pathogenic varaint. ACMG criteria used for classification: PVS1, PM2. |