Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001420850 | SCV001623260 | benign | not specified | 2021-05-03 | criteria provided, single submitter | clinical testing | Variant summary: CACNA1C c.4623+13G>A alters a non-conserved nucleotide located close to a canonical splice site and therefore could affect mRNA splicing, leading to a significantly altered protein sequence. 4/4 computational tools predict no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant allele was found at a frequency of 0.00074 in 230660 control chromosomes, predominantly at a frequency of 0.0065 within the African or African-American subpopulation in the gnomAD database. The observed variant frequency within African or African-American control individuals in the gnomAD database is approximately 650 fold of the estimated maximal expected allele frequency for a pathogenic variant in CACNA1C causing Timothy Syndrome phenotype (1e-05), strongly suggesting that the variant is a benign polymorphism found primarily in populations of African or African-American origin. To our knowledge, no occurrence of c.4623+13G>A in individuals affected with Timothy Syndrome and no experimental evidence demonstrating its impact on protein function have been reported. No clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014. Based on the evidence outlined above, the variant was classified as benign. |
Gene |
RCV001711912 | SCV001945195 | benign | not provided | 2015-03-03 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002056287 | SCV002402789 | benign | Long QT syndrome | 2024-01-28 | criteria provided, single submitter | clinical testing | |
Breakthrough Genomics, |
RCV001711912 | SCV005234715 | benign | not provided | criteria provided, single submitter | not provided |