Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002380403 | SCV002670466 | uncertain significance | Cardiovascular phenotype | 2018-05-01 | criteria provided, single submitter | clinical testing | The p.R246Q variant (also known as c.737G>A), located in coding exon 5 of the CACNA1C gene, results from a G to A substitution at nucleotide position 737. The arginine at codon 246 is replaced by glutamine, an amino acid with highly similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be deleterious by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Gene |
RCV003317598 | SCV004021490 | pathogenic | not provided | 2023-01-19 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Not observed at significant frequency in large population cohorts (gnomAD) |