Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004700252 | SCV005201743 | pathogenic | not provided | 2023-08-10 | criteria provided, single submitter | clinical testing | Published transgenic mouse and rat models harboring this variant demonstrate spontaneous seizures during periods of increased EEG delta wave activity which would correlate with slow-wave sleep in humans (Manfredi et al., 2009; Shiba et al., 2015); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 19237585, 20603624, 11062464, 27336596, 25565544, 28717674, 11512019, 15245761, 23934645, 18342259, 33924731, 15843070, 17662253, 12015163, 22897520, 21704022, 36835631, 17900292, 26072248, 21091316, 12681012, 12773798, 11952766, 15130686, 33689168, 23123803, 26309560, 33284031, 28761347, 33255633, 26561946, 35513164, 11893908, 16815873, 36796465, 12887446, 12782965, 12823585, 25104926, 11579434, 26091610, 11904236, 19153075) |
Department of Neurology, |
RCV000019047 | SCV005889667 | pathogenic | Autosomal dominant nocturnal frontal lobe epilepsy 3 | 2025-01-08 | criteria provided, single submitter | clinical testing | PS3, PM1, PM5, PM2_Supporting+PS4_Supporting |
OMIM | RCV000019047 | SCV000039334 | pathogenic | Autosomal dominant nocturnal frontal lobe epilepsy 3 | 2000-11-01 | no assertion criteria provided | literature only |