Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000192555 | SCV000247037 | uncertain significance | not specified | 2014-12-02 | criteria provided, single submitter | clinical testing | |
Gene |
RCV002243875 | SCV002513596 | likely pathogenic | not provided | 2022-02-08 | criteria provided, single submitter | clinical testing | Intronic +5 splice site variant in a gene for which loss-of-function is a known mechanism of disease, and splice predictors support a deleterious effect; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 32978031, 27241786) |